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Table 3 Histological characteristics

From: Severe combined immunodeficiency: improved survival leading to detection of underlying liver disease

Patient

Characteristic

NAS

Fibrosis Stage

Steatosis Grade

Ballooning Grade

3

Steatohepatitis

3

2-PPF + PSF

1

1

5

Normal liver parenchyma

6

Hepatoblastoma, normal uninvolved liver parenchyma

7

Steatosis

1

0-NF

1

0

11

Steatosis

2

1-PPF

1

0

15

Steatohepatitis

4

3-BF

2

1

17

Zone 1 borderline

3

3-BF

2

0

18

Zone 1 borderline

3

2-PPF + PSF

2

0

  1. NAS: NAFLD activity score
  2. NF: No fibrosis
  3. PPF: Periportal fibrosis
  4. PSF: Perisinusoidal fibrosis
  5. BF: bridging fibrosis
  6. 1: PPF
  7. 2: PPF + PSF