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Table 2 Summary of 19 cases with JXG involving the Pancreas

From: Pancreatic involvement in Erdheim-Chester disease: a case report and review of the literature

No. References

Sex/age

Symptoms

Site

Treatment

Outcome

Other organs involved

1. Dehner [21]

M/2mo

Jaundice

Head

Unknown

Resolution

Lung

2. Heintz et al. [22]

F/5mo

Jaundice

Head

Whipple

Resolution

Liver

3. Prasil et al. [23]

NA/9mo

Jaundice

Head

Mass excision

Resolution

–

4. Ueno et al. [24]

M/42y

Belly pain

Body (cyst)

Distal pancreatectomy

Resolution

–

5. Iyer et al. [25]

M/50y

Jaundice

Head

Whipple

Unknown

Unknown

6. Iyer et al. [25]

M/36y

Pancreatitis

Tail

Mass excision

Unknown

Unknown

7. Kamitani et al. [26]

M/82y

Belly pain

Body (cyst)

Whipple

Unknown

Stomach

8. Kang 2007

F/22y

Belly pain

Head

PPPD

Unknown

Unknown

9. Okabayashi et al. [27]

M/60y

Belly pain

Tail

Distal pancreatectomy

Unknown

Unknown

10. Okabayashi et al. 2007

M/69y

Belly pain

Tail

Distal pancreatectomy

Unknown

Unknown

11. Shima et al. [28]

M/66y

Belly pain

Body

Distal pancreatectomy

Unknown

–

12. Iso et al. [29]

M/82y

Weight loss

Head and tail

Distal pancreatectomy

Resolution

Spleen

13. Ikeura et al. [30]

M/73y

–

Body (cyst)

PPPD

Unknown

–

14. Uguz et al. [31]

M/30y

Belly pain

Head

PPPD

Unknown

Unknown

15. Uguz et al. [31]

M/34y

Belly pain

Head

PPPD

Unknown

Unknown

16. Kim et al. [32]

F/72y

Weight loss

Body (cyst)

PPPD

Resolution

–

17. Kim et al. [33]

F/70y

Belly pain, dyspepsia

Uncinate

Whipple

Resolution

–

18. Atreyapurapu et al. [34]

M/60y

Belly pain, vomit

Uncinate

Whipple

Resolution

–

19. Antary et al. [35]

F/13mo

Jaundice

Head and uncinate

Whipple

Resolution

–

  1. PPPD pylorus preserving pancreatoduodenectomy