From: Safety and outcome of gastrostomy tube placement in patients with Loeys-Dietz syndrome
Patient | LDS Type | Sex | Comorbidities† | Technique* | age at placement§ | Indication | BMI Z-score at placement | BMI ∆ Z-score/ month** | years follow up | Most recent BMI Z-score ‡ |
---|---|---|---|---|---|---|---|---|---|---|
1 | 1 | M | FA, EGID, crohns | PEG 14F | 10 | FTT | −2.32 | −0.37 | 10.4 | −6.90 |
2.1 | 1 | M | Open | < 1 | Poor intake | −1.96 | −0.04 | 0.9 | ||
2.2 | PEG 20F | 3 | FTT | −3.63 | 0.84 | 5.2 | −2.99 | |||
3 | 1 | M | Lap w/BIH | < 1 | FTT, poor intake | −2.78 | 0.18 | 2.1 | −1.71 | |
4 | 1 | M | Lap w/LIH | 7 | FTT | −7.04 | 0.45 | 0.7 | −3.45 | |
5.1 | 1 | F | FA, eczema | Lap w/Nissen, Ladds for malrotation | 8 | FTT | −2.10 | −0.36 | 0.7 | |
5.2 | Lap | 10 | FTT | −4.25 | 0.02 | 7.3 | −1.97 | |||
6 | 2 | M | Lap | 9 | FTT | −4.25 | 0.12 | 8.6 | 0.34 | |
7 | 2 | F | FA, EGID, UC | PEG 14F | 13 | FTT | −2.53 | −0.25 | 1.1 | −3.96 |
8 | 2 | F | FA, EGID | PEG 16F | 5 | FTT | −1.45 | −0.03 | 9.6 | −0.46 |
9 | 2 | F | FA, EGID | Open, Stamm w/Nissen | < 1 | Poor intake | −1.56 | 0.29 | 13.7 | 0.54 |
10 | 2 | F | EGID | PEG 20F | 7 | FTT | −5.40 | 0.78 | 0.6 | −0.80 |
Median | 7 | −2.66 | 0.07 | 6.2 | −1.84 | |||||
Minimum | < 1 | −7.04 | −0.37 | 0.6 | −6.90 | |||||
Maximum | 13 | −1.45 | 0.84 | 13.7 | 0.54 |