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Table 1 Risk factors of portal vein thrombosis in all patients (n = 67)

From: Portal vein thrombosis; risk factors, clinical presentation and treatment

Primary risk factor

All risk factors

Prothrombotic disorder n = 19 (28%)

Prothrombotic disorder n = 36 (54%)

Hyperhomocysteinemia (n = 13), antiphospholipid syndrome (n = 9), hormone replacement therapy (n = 2), Factor V Leiden mutation (n = 3), Protein C deficiency (n = 2), Polycythaemia vera (n = 2), myeloproliferative syndrome (n = 1), Protein S deficiency (n = 1), antitrombin III deficiency (n = 1), disseminated coagulation (n = 1), essential thrombocytosis (n = 1)

Abdominal inflammation n = 13 (19%)

Abdominal inflammation n = 23 (34%)

Chronic pancreatitis (n = 11), Cholangitis (n = 5), acute pancreatitis (n = 2), liver abscesses (n = 2), umbilical vein catheterization (n = 1), cholecystolithiasis (n = 1), polycystic liver disease (n = 1)

Cirrhosis n = 9 (13%)

Cirrhosis n = 12 (18%)

Cancer n = 7 (11%)

Cancer n = 9 (13%)

Neuro-endocrine Tumor (n = 4)*, hepatocellular carcinoma (n = 2), pancreatic cancer (n = 1), unknown primary tumour (n = 1), angiomyxoma (n = 1)

Abdominal intervention n = 5 (8%)

Abdominal intervention n = 8 (12%)

Splenectomy (n = 3), cholecystectomy (n = 2), Billroth II (n = 1), radiofrequency ablation (n = 1), gastropancreaticcystotomy (n = 1)

Abdominal infection n = 5 (8%)

Abdominal infection n = 9 (13%)

Bacteraemia (n = 4), portal vein phlebitis (n = 2), intestinal tuberculosis (n = 1), sepsis (n = 1), tuberculosis in psoas abscess (n = 1)

Idiopathic n = 9 (13%)

Idiopathic n = 9 (13%)

  1. * A relative large proportion reflecting the centre's specialist function for this disease. Patients can have more than one risk factor.