Table 1 Summary of 5 cases with ECD and LCH involving the Pancreas
From: Pancreatic involvement in Erdheim-Chester disease: a case report and review of the literature
No. References | Sex/age | Symptoms | Site | Treatment | Outcome | Other organs involved |
|---|---|---|---|---|---|---|
1. Poehling et al. [13] | F/57y | Cramping | Autopsy | Prednisone | Death | Bone, kidney |
2.Hara et al. [16] | M/10y | Fever, jaundice | Diffuse swelling | Chemo (EP) | Death | Lung, liver, spleen, BM, kidney |
3.Yu et al. [17] | M/8mo | Belly pain, distension, diarrhea | Autopsy | Chemo (VP,C) | Death | Skin, liver, spleen, BM, lung, GI |
4.Muwakkit et al. [18] | M/4w | Frequent stools | Body (cyst) | Chemo (VP) | Resolution | Skin, lung, spleen |
5.Goyal et al. [19] | M/18mo | Loose stools | Autopsy | Chemo (VP) | Death | LN, liver, kidney |
6.Hou et al. [20] | M/44y | / | Diffuse swelling | Chemo (CAVP) | Resolution | Lung, liver, LN, bone |