PAA | NICCD (n=4) median (range) | Non-NICCD (n=18) median (range) | Normal value | P-valueb |
---|---|---|---|---|
Citrulline (umol/L) | 60 (36-152) | 17 (8-42) | 3-35 | 0.004 |
Methionine (umol/L) | 141 (32-243) | 37 (11-702) | 9-42 | 0.23 |
Phenylalanine (umol/L) | 38 (26-40) | 45 (11-291) | 31-75 | 0.19 |
Threonine (umol/L) | 181 (139-326) | 140 (42-339) | 24-174 | 0.11 |
Arginine (umol/L) | 63 (50-135) | 41 (12-92) | 12-133 | 0.16 |
Tyrosine (umol/L) | 121 (33-166) | 74 (18-557) | 22-108 | 0.49 |
Threonine/serine ratioa | 1.63 (1.37-2.10) | 1.16 (0.56-2.30) | 1.10 (0.88-1.19) | 0.03 |
Fisher ratio (BCAA/AAA) | 1.12 (0.67-2.47) | 2.23 (0.01-3.42) | 3.42±0.33 | 0.13 |