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Table 3 Summary of 11 cases with RDD involving the Pancreas

From: Pancreatic involvement in Erdheim-Chester disease: a case report and review of the literature

No. References

Sex/age

Symptoms

Site

Treatment

Outcome

Other organs involved

1. Esquivel et al. [36]

F/48y

Belly pain

Body and tail

Distal pancreatectomy

Unknown

Spleen

2. Zivin et al. [37]

F/63y

Jaundice

Body

Whipple

Resolution

Lung

3. Podberezin et al. [38]

F/35y

Belly pain

Tail

Mass excision

Progression (steroids, chemo, imatinib, excision)

Spine, perinephric, perisplenic

4. Romero et al. [39]

F/74y

Belly pain

Head

PPPD

Unknown

–

5. Shaikh et al. [40]

F/59y

Belly pain

Body and tail

Whipple, steroids

Progression (imatinib)

Liver

6. Mantilla et al. [41]

F/54y

Belly pain, weight loss

Tail

Distal pancreatectomy

Resolution

–

7. Karajgikar et al. [42]

F/65y

Belly pain

Head, body, and tail

Consider clofarabine

Unknown

Presacral soft tissue, skin

8. Smith et al. [43]

F/75y

Weight loss

Body

Steroids

Resolution

–

9. Brown et al. [44]

F/65y

Granulomatous uveitis, skin rash

Tail

Distal pancreatectomy

Resolution

Skin

10. Liu et al. [45]

F/71y

Fullness

Tail

Distal pancreatectomy

Resolution

–

11. Emily et al. [46]

F/40y

Belly pain

Tail

Distal pancreatectomy

Resolution

Colon