Table 1 Cases of undifferentiated embryonal sarcoma of the liver with large-sized tumors
References | Age (year), Sex | Tumor size/weight | Treatment | Follow-up |
|---|---|---|---|---|
Baron et al. [8] | 13, male | 25 cm, 3 kg | Right hepatic trisegmentectomy, postoperative chemotherapy (six cycles: cisplatin and adriamycin with vincristine, ifosfamide, and etoposide) | 48 months tumor-free following the treatment |
Kamrani et al. [9] | 11, female | 25 × 19 × 14 cm (on T2-weighted MRI) | Left lateral hepatectomy | (not mentioned) |
Plumblee et al. [10] | 8, male | 21 × 14 cm (the largest size observed in imaging) | Neoadjuvant chemotherapy (one cycle: vincristine, actinomycin D, cyclophosphamide; three cycles: ifosfamide/doxorubicin), orthotopic liver transplant, adjuvant chemotherapy (two cycles: ifosfamide/doxorubicin; one cycle: ifosfamide) | Well at 18 months post-transplant |
Bahador et al. (our case) | 13, female | 28 × 20 × 12 cm (weighing 5 kg) | Exploratory laparotomy followed by right hepatectomy | 6 years tumor-free |