From: Role of percutaneous liver biopsy in infantile cholestasis: cohort from Arabs
Age at LB (days) | Histology on percutaneous LB | Wedge LB | US liver | MRI liver | IOC | |
---|---|---|---|---|---|---|
1 | 60 | No significant BD proliferation. No BD plugs. BD injury with few vanished BD. Moderate portal fibrosis. Canalicular cholestasis. Pathologist suggested neonatal sclerosing cholangitis | Marked BD proliferation. BD plugs. BD injury not seen. Fibrous septae and marked portal fibrosis | CBD visualized. Normal GB size | Hypoplastic GB | Failed due to atrophic GB |
2 | 90 | Mild BD proliferation. No BD plugs. Marked portal fibrosis with septae. Hepatocytes swelling. GC transformation. Canalicular cholestasis. Pathologist suggested BASD and PFIC 2 | ND | CBD non-visualized Echogenic cord sign GB non-visualized | CBD non-visualized GB non-visualized | ND* |
3‡ | 60 | Mild BD proliferation. No BD plugs. Marked portal fibrosis with septae. Hepatocytes ballooning. Canalicular cholestasis. Pathologist suggested BASD and PFIC 3 | ND | CBD non-visualized GB atrophic | CBD non-visualized GB non-visualized | ND* |