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Table 2 The histological description of the 3 confirmed biliary atresia cases mislabeled as non-BA

From: Role of percutaneous liver biopsy in infantile cholestasis: cohort from Arabs

 

Age at LB (days)

Histology on percutaneous LB

Wedge LB

US liver

MRI liver

IOC

1

60

No significant BD proliferation. No BD plugs. BD injury with few vanished BD. Moderate portal fibrosis. Canalicular cholestasis. Pathologist suggested neonatal sclerosing cholangitis

Marked BD proliferation. BD plugs. BD injury not seen. Fibrous septae and marked portal fibrosis

CBD visualized. Normal GB size

Hypoplastic GB

Failed due to atrophic GB

2

90

Mild BD proliferation. No BD plugs. Marked portal fibrosis with septae. Hepatocytes swelling. GC transformation. Canalicular cholestasis. Pathologist suggested BASD and PFIC 2

ND

CBD non-visualized

Echogenic cord sign

GB non-visualized

CBD non-visualized

GB non-visualized

ND*

3

60

Mild BD proliferation. No BD plugs. Marked portal fibrosis with septae. Hepatocytes ballooning. Canalicular cholestasis. Pathologist suggested BASD and PFIC 3

ND

CBD non-visualized

GB atrophic

CBD non-visualized

GB non-visualized

ND*

  1. LB liver biopsy, US ultrasound, MRI magnetic resonance image, IOC intraoperative cholangiogram, BD bile ducts, CBD common bile duct, GB gall bladder, GC giant cell, BASD bile acid synthesis disorder, PFIC progressive familial intrahepatic cholestasis, ND not done, ND* not done because of late presentation, the child underwent liver transplantation and biliary atresia was confirmed intraoperatively
  2. Patient has heterotaxy syndrome, intrahepatic interruption of inferior vena cava, hemi-azygous continuation, and the superior mesenteric vein was seen anterior to the superior mesenteric artery