Table 1 Clinical profiles of the 17 patients with IgG4-SC
Characteristics | Values |
|---|---|
Age (years) | 63 (51–77) |
Sex (male: female) | 16: 1 |
Serological findings | |
 Serum IgG4 (mg/dL) | 264 (21–2590) |
 Elevated serum IgG4 level (≥135 mg/dL), n (%) | 15 (88%) |
 Serum IgG (mg/dL) | 1543 (807–5530) |
 Total bilirubin (mg/dL) | 1.2 (0.6–22.4) |
 ALP (IU/L) | 677 (107–1331) |
 CA19–9 (U/L) | 10 (0–107) |
Cholangiographic classification, n (%) | |
 Type 1 | 7 (41%) |
 Type 2 | 0 (0%) |
 Type 3 | 2 (12%) |
 Type 4 | 8 (47%) |
Other organ involvement, n (%) | 15 (88%) |
 Autoimmune pancreatitis | 15 (88%) |
 Sclerosing dacryoadenitis & sialadenitis | 3 (18%) |
 Retroperitoneal fibrosis | 1 (6%) |
Diagnosis, n (%) | |
 Definite | 15 (88%) |
 Probable | 1 (6%) |
 Possible | 1 (6%) |
Steroid therapy, n (%) | 14 (82%) |