From: Small bowel adenocarcinoma as a complication of celiac disease: clinical and diagnostic features
Case # | Sex | HLA | Age at CD diagnosis (yrs) | Age at SBA diagnosis (yrs) | SBA localization | TNM at diagnosis | Presentation | Key diagnostic exam(s) for SBA | Chemotherapy | Survival at 6 years |
---|---|---|---|---|---|---|---|---|---|---|
1 | F | DQ2 | 68 | 72 | Jejunum | T3N0M0 | Acute intestinal obstruction | Abdominal X-ray; double contrast upper GI radiography; Exploratory laparotomy | None | Alive |
2 | F | DQ2 homozygosis | 34 | 69 | Jejunum | T2N0M0 | Iron deficiency anaemia | VCE; DBE | None | Alive |
3 | F | DQ2 | 46 | 46 | Jejunum | T4N2M2 | Intestinal sub-occlusion | Small bowel loop ultrasound; CT enteroclysis | FOLFOX + Bevacizumab | Dead after 13 months |
4 | F | DQ2 | 38 | 38 | Jejunum | T3N2M0 | Intestinal sub-occlusion | CT scan; PET; DBE | FOLFOX | Alive |
5 | F | DQ2 | 40 | 40 | Duodenum | T3N2M0 | Abdominal pain | OGD | FOLFOX + FOLFIRI | Dead after 63 months |