Pts | Gender | Age at diagnosis (yrs) | Clinical phenotype | HLA | Delay in CD diagnosis (yrs) | Age at complication (yrs) | Complication | Outcome |
---|---|---|---|---|---|---|---|---|
#1 | M | 42 | Classical | DQ2 + ° | 8 | 45 | EATCL | Alive, 54 yrs |
#2 | F | 66 | Classical | DQ2+ | 10 | 70 | RCD type 1 | Alive, 73 yrs |
#3 | F | 52 | Classical | DQ2 + ° | 5 | 56 | RCD type 1 | Alive, 64 yrs |
#4 | F | 48 | Classical | DQ2+ | 6 | 51 | Small bowel carcinoma | Dead, 53 yrs |
#5 | F | 65 | Classical | DQ2 + ° | 11 | 65 | Small bowel carcinoma | Alive, 76 yrs |
#6 | F | 55 | Classical | DQ2+ | 7 | 59 | RCD type 1 | Alive, 66 yrs |