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Table 2 Liver Histology prior to Partial External Biliary Diversion

From: Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion

  

Fibrosis

Parenchyma

Pt

Disease

Portal

Pericellular

Cholestasis

Pseudoacini

Ballooning

1

AGS

2

1

2

0

0

2

AGS

NA

NA

NA

NA

NA

3

AGS

NA

NA

NA

NA

NA

4

FIC1 disease

2

1

0

0

0

5

FIC1 disease

3

3

1

0

0

6

FIC1 disease

2

1

3

0

2

7

FIC1 disease

3

1

2

1

0

8

BSEP disease

4

1

2

2

0

9

BSEP disease

2

1

3

1

1

10

BSEP disease

2

2

3

0

0

  1. Non-responders are in bold and italics
  2. NA = not available because liver biopsy not performed at time of PEBD.