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Table 1 Non-exocrine clinical features considered part of 1°SS for this study (excluding liver)

From: The liver is a common non-exocrine target in primary Sjögren's syndrome: A retrospective review

1

Lung

Lymphocytic interstitial pneumonia, fibrosing alveolitis, pseudolymphoma, lymphoma, pulmonary amyloidosis

2

Renal

Renal tubular acidosis type I, nephrogenic diabetes insipidus, chronic interstitial nephritis, immune-mediated glomerulonephritis

3

Cardiovascular

Myocarditis, pericarditis, pericardial effusion, Raynaud's

4

Gastrointestinal

Atrophic gastritis, pancreatitis

5

Vasculitis

Mononeuritis multiplex, axonal neuropathy, purpura

6

Hematologic

Coombs positive hemolytic anemia, leukopenia, lymphopenia, thrombocytopenia, hypoplasic bone marrow

7

Peripheral nervous system

Axonal neuropathy, mononeuritis multiplex

8

Central nervous system

Aseptic meningitis, cerebral vasculitis, CVA, TIAs, multiple sclerosis "like" changes

9

Endocrine

Autoimmune thyroid disease

10

Musculoskeletal

Arthritis, arthralgias, myositis

  1. CVA: central vascular accident TIA: transient ischemic attack