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Table 3 Clinical characteristics of patients suspected of AIP but who did not meet diagnostic criteria

From: IgG4 Related disease – a retrospective descriptive study highlighting Canadian experiences in diagnosis and management

Patient characteristic PSC and elevated IgG4 Radiological changes c/w AIP
Number of patients 4 5
   Males (n, %) 4 (100%) 4 (80%)
   Age (years, mean) 63 54
IgG4 (g/L, median) 7.3 NA
IgG4 > 2 × ULN (n, %) 4
Biochemistry
   Bilirubin (μmol/L*) 11.0 (11–124) 47.0 8–217)
   ALP (U/L*) 330.0 (71–1500) 204.0 (100–303)
   ALT (U/L*) 62.0 (23–234) 91.0 (29–115)
   AST (U/L*) 54.5 (17–229) 41.5 (21–94)
Presentation
   Obstructive jaundice 1 4
   Weight loss 2 4
   Abdominal pain 2 5
Imaging modality
   CT (n, %) 3 5
   MRCP (n, %) 4 5
   ERCP (n, %) 2 4
Radiological pancreatic parenchyma typical
   Diffuse 0 4
   Multifocal 0 0
   Peripheral rim enhancement 1 4
(Halo) 1 1
Atypical
Focal 0 0
   Atrophic
AIP Radiological classification
   SC 3 0
   SP-SC 0 3
   SP 0 2
Biliary changes
   Intrahepatic duct 4 2
   Proximal extra-hepatic duct 2 4
Initial treatment
   Steroids 3 0
   ERCP and biliary stenting 0 4
   Steroids and biliary stenting 0 0
   Response to steroids 1 0
Complications
   Cholangiocarcinoma 1 0
  1. *Median.