Diagnostic factors n = 27 (49%) | All criteria met | HISORt (2006) n = 30, (55%) | Japanese (2006) n = 31 (56%) | Korean (2007) n = 45 (82%) | No criteria met n = 9 (16%) |
---|---|---|---|---|---|
I. Typical imaging | 20 (74%) | 21 (70%) | 20 (65%) | 27 (60%) | 4 (44%) |
Ia. Atypical imaging | 7 (26%) | 9 (30%) | 11 (35%) | 18 (40%) | 2 (22%) |
II. Lab IgG4 | 21 (81%) | 23 (77%) | 26 (84%) | 26 (58%) | 3 (33%) |
III. Histology | 7 (30%) | 8 (27%) | 8 (26%) | 8 (18%) | 0 (0.0%) |
IV. Other organ involvement | 18 (70%) | 22 (73%) | 21 (68%) | 28 (62%) | 2 (22%) |
V. Steroid response | 14 (52%) | 17 (57%) | 14 (45%) | 23 (51%) | 1 (11%) |
Definite diagnosis | |||||
- | III (8) | I + II (17) | I + II (18) | - | |
Ia + II (8) | |||||
- | I + II (18) | Ia + II (9) | I + III (3) | - | |
Ia + III (2) | |||||
- | Ia + II + V (2) | I + III (3) | I + IV (4) | - | |
Ia + IV (2) | |||||
- | Ia + IV + V (2) | Ia + III (2) | I + V (5) | - | |
Ia + V (3) |