Report | Age (yrs), Sex | Dx | Splenomegaly | Thrombocytopenia | Leucopenia | Gastric varices | Esophageal varices | Encephalopathy | Ab-normal Liver function tests | Liver transplantation | Portal fibrosis | Vascular changes | Inflammation/heaptitis | Follow-up | Recovery |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Upshaw (1979) [19] | 46, M | AI | yes | yes | yes | no | yes | no | no | no | yes | no | no | 12 yr | yes |
Lindor (1987) [18] | 65, M | Ly | yes | yes | yes | no | yes | no | (yes) | no | no | no | no | 14 mo | yes |
Petrowsky (1997) [8] | 30, M | None | yes | yes | yes | no | yes | no | yes | yes | yes | yes | no | 26 mo | yes |
Sasajima (2006) [10] | 53, F | RA | yes | yes | no | yes | no | no | yes | no | no | yes | yes | 12 mo | yes |
Ohta (2001) [11] | 59, M | None | NA | NA | NA | NA | NA | yes | NA | no | yes | no | no | NA | yes |
Inagaki (2000) [12] | 38, M | SLE | yes | yes | yes | no | yes | no | yes | no | yes | no | yes | 24 mo | yes |
Ziarkiewicz (2004) [9] | 21, M | None | yes | yes | yes | no | no | no | NA | no | yes | yes | no | 6 mo | yes |
Bernard (1995) [14] | 20, M | None | yes | yes | yes | no | no | no | NA | yes | yes | no | no | 14 yr | yes |
Yoshimura (1994) [15] | 30, M | RTx | yes | yes | yes | no | yes | no | no | no | yes | no | yes | 6 yr | yes |
Yoshimura (1994) [15] | 22, M | RTx | yes | yes | yes | no | yes | no | no | no | yes | no | no | 26 mo | yes |
Tsujimura (1987) [16] | NA | PHI | NA | NA | NA | NA | NA | no | no | no | no | yes | yes | NA | no |
Babbs (1991) [17] | 30, M | IgAN | yes | no | no | no | yes | no | no | no | no | no | no | 30 mo | yes |
Noël (1995) [13] | 36, M | RTx | yes | yes | yes | no | yes | no | no | no | yes | no | no | 12 mo | yes |
Treška (2005) [7] | 20, M | None | yes | yes | yes | no | no | no | no | no | no | no | yes | 10 mo | yes |
Our Case | 0.7, M | None | yes | yes | yes | no | no | no | no | no | no | no | no | 18 mo | yes |