Skip to main content

Table 2 Case Reports of Splenectomy In Idiopathic Portal Hypertension.

From: Life-threatening hypersplenism due to idiopathic portal hypertension in early childhood: case report and review of the literature

Report

Age (yrs), Sex

Dx

Splenomegaly

Thrombocytopenia

Leucopenia

Gastric varices

Esophageal varices

Encephalopathy

Ab-normal Liver function tests

Liver transplantation

Portal fibrosis

Vascular changes

Inflammation/heaptitis

Follow-up

Recovery

Upshaw (1979) [19]

46, M

AI

yes

yes

yes

no

yes

no

no

no

yes

no

no

12 yr

yes

Lindor (1987) [18]

65, M

Ly

yes

yes

yes

no

yes

no

(yes)

no

no

no

no

14 mo

yes

Petrowsky (1997) [8]

30, M

None

yes

yes

yes

no

yes

no

yes

yes

yes

yes

no

26 mo

yes

Sasajima (2006) [10]

53, F

RA

yes

yes

no

yes

no

no

yes

no

no

yes

yes

12 mo

yes

Ohta (2001) [11]

59, M

None

NA

NA

NA

NA

NA

yes

NA

no

yes

no

no

NA

yes

Inagaki (2000) [12]

38, M

SLE

yes

yes

yes

no

yes

no

yes

no

yes

no

yes

24 mo

yes

Ziarkiewicz (2004) [9]

21, M

None

yes

yes

yes

no

no

no

NA

no

yes

yes

no

6 mo

yes

Bernard (1995) [14]

20, M

None

yes

yes

yes

no

no

no

NA

yes

yes

no

no

14 yr

yes

Yoshimura (1994) [15]

30, M

RTx

yes

yes

yes

no

yes

no

no

no

yes

no

yes

6 yr

yes

Yoshimura (1994) [15]

22, M

RTx

yes

yes

yes

no

yes

no

no

no

yes

no

no

26 mo

yes

Tsujimura (1987) [16]

NA

PHI

NA

NA

NA

NA

NA

no

no

no

no

yes

yes

NA

no

Babbs (1991) [17]

30, M

IgAN

yes

no

no

no

yes

no

no

no

no

no

no

30 mo

yes

Noël (1995) [13]

36, M

RTx

yes

yes

yes

no

yes

no

no

no

yes

no

no

12 mo

yes

Treška (2005) [7]

20, M

None

yes

yes

yes

no

no

no

no

no

no

no

yes

10 mo

yes

Our Case

0.7, M

None

yes

yes

yes

no

no

no

no

no

no

no

no

18 mo

yes

  1. M, Male; F, Female; Dx, Accompanying Disease; AI, Arsenic Ingestion; Ly, Lymphoma; RA, Rheumatoid Arthritis; SLE, Systemic Lupus Erythematosus; RTx, Renal Transplantation; PHI, Polyclonal Hyperimmunglobulinemia; IgAN, IgA Nephropathy; Mo, Months; Yr, Years; NA, Data not available.